Hydrocephalus in mucopolysaccharidosis Type VI successfully treated with endoscopic third ventriculostomy
Mucopolysaccharidosis (MPS) Type VI, or Maroteaux-Lamy syndrome, is characterized by a deficiency of the enzyme arylsulfatase B (ASB). In patients with this disorder, craniocervical compression, carpal tunnel syndrome, and communicating hydrocephalus are common. Traditionally, hydrocephalus occurrin...
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Formato: | article |
Idioma: | pt_BR |
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Journal of Neurosurgery: Pediatrics
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Endereço do item: | https://repositorio.ufrn.br/handle/123456789/52354 |
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