Hydrocephalus in mucopolysaccharidosis Type VI successfully treated with endoscopic third ventriculostomy

Mucopolysaccharidosis (MPS) Type VI, or Maroteaux-Lamy syndrome, is characterized by a deficiency of the enzyme arylsulfatase B (ASB). In patients with this disorder, craniocervical compression, carpal tunnel syndrome, and communicating hydrocephalus are common. Traditionally, hydrocephalus occurrin...

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Detalhes bibliográficos
Principais autores: Silva Neto, Ângelo Raimundo da, Holanda, Gervina Brady Moreira, Farias, Maria Cláudia Saldanha, Costa, Gladstone Santos da, Pereira, Hougelle Simplício Gomes
Outros Autores: https://orcid.org/0000-0002-3819-8951
Formato: article
Idioma:pt_BR
Publicado em: Journal of Neurosurgery: Pediatrics
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Endereço do item:https://repositorio.ufrn.br/handle/123456789/52354
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